All are true regarding Caroli’s disease except? – Surgery MCQ

All are true regarding Caroli’s disease except?
A. Intrahepatic stone formation
B. Biliary stasis
C. Commonly presents with ascites
D. Malignant change can occur

Correct answer : C. Commonly presents with ascites

CT scan of cholangiocarcinoma. Malignant change can occur in Caroli’s disease.

• Caroli’s disease is congenital dilatation of the intrahepatic biliary tree.
• This disease is complicated by presence of intrahepatic stone formation.
• Patients can present with abdominal pain or sepsis.
• Biliary stasis with stone formation can lead to biliary sepsis.
• Malignant change in the ductal system can lead to cholangiocarcinoma.

Ref: Bailey and Love’s Short Practice of Surgery, 25th edition, p 1093.
Image credits: Samir. https://en.wikipedia.org/wiki/File:CT_cholangioca.jpg