Lymphangiosarcoma was originally described in? – Surgery MCQ

Lymphangiosarcoma was originally described in?
A. Stewart-Treves’ syndrome
B. Klippel-Trenaunay’s syndrome
C. Milroy’s disease
D. Meig’s disease

Correct answer : A. Stewart-Treves’ syndrome

  • Lymphangiosarcoma was originally described in Stewart-Treves’ syndrome (post mastectomy lymphoedema).
  • It affects about 0.5% of patients.
  • Stewart and Treves reported this in a joint paper in 1948.
  • Milroy’s disease is familial lymphoedema type 1.
  • Meig’s disease is familial lymphoedema type 2.

Ref: Bailey and Love’s Short Practice of Surgery, 25th edition, p 948-950.