Right sided isomerism – Paediatrics MCQ
Right sided isomerism is found in association with?
A. Asplenia
B. Single spleen
C. Two spleens
D. Multiple spleens
Correct answer : A. Asplenia
Right sided isomerism
- Alternate names – Ivemark syndrome / asplenia syndrome
- It is a type of situs anomaly
- Features : asplenia, malrotation of bowel, transverse liver, gall bladder agenesis, imperforate anus, horseshoe adrenal gland, urethral valves
- The patients are immunocompromised due to absence of spleen, most die before 1 year of age