Right sided isomerism – Paediatrics MCQ

Right sided isomerism is found in association with?

A. Asplenia
B. Single spleen
C. Two spleens
D. Multiple spleens

Correct answer : A. Asplenia

Right sided isomerism

  • Alternate names – Ivemark syndrome / asplenia syndrome
  • It is a type of situs anomaly
  • Features : asplenia, malrotation of bowel, transverse liver, gall bladder agenesis, imperforate anus, horseshoe adrenal gland, urethral valves
  • The patients are immunocompromised due to absence of spleen, most die before 1 year of age